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Concept information

Preferred term

Creutzfeldt-Jakob Syndrome  

Type

  • Topical Descriptor

Broader concept

Entry terms

  • CJD (Creutzfeldt Jakob Disease)
  • CJD (Creutzfeldt-Jakob Disease)
  • Creutzfeldt Jacob Disease
  • Creutzfeldt Jakob Disease
  • Creutzfeldt-Jakob Disease
  • Disease, Creutzfeldt Jacob
  • Disease, Creutzfeldt-Jakob
  • Disease, Jakob-Creutzfeldt
  • Encephalopathies, Subacute Spongiform
  • Encephalopathy, Subacute Spongiform
  • Jacob Disease, Creutzfeldt
  • Jakob Creutzfeldt Disease
  • Jakob-Creutzfeldt Disease
  • Jakob Creutzfeldt Syndrome
  • Jakob-Creutzfeldt Syndrome
  • Spongiform Encephalopathies, Subacute
  • Spongiform Encephalopathy, Subacute
  • Subacute Spongiform Encephalopathies
  • Subacute Spongiform Encephalopathy
  • Syndrome, Jakob-Creutzfeldt

Scope note

  • A rare transmissible encephalopathy most prevalent between the ages of 50 and 70 years. Affected individuals may present with sleep disturbances, personality changes, ATAXIA; APHASIA, visual loss, weakness, muscle atrophy, MYOCLONUS, progressive dementia, and death within one year of disease onset. A familial form exhibiting autosomal dominant inheritance and a new variant CJD (potentially associated with ENCEPHALOPATHY, BOVINE SPONGIFORM) have been described. Pathological features include prominent cerebellar and cerebral cortical spongiform degeneration and the presence of PRIONS. (From N Engl J Med, 1998 Dec 31;339(27))

History note

  • 1991; use JAKOB-CREUTZFELDT SYNDROME 1981-1990, use CREUTZFELDT-JAKOB DISEASE 1969-1980

In other languages

  • Finnish

  • CJD
  • Creutzfeld-Jakob disease
  • Creutzfeldt
  • Creutzfeldt-Jakob
  • Creutzfeldt-Jakobin oireyhtymä
  • Creutzfeldt-Jakobin syndrooma
  • encephalopathia spongiformis subacuta
  • Jacob-Creutzfeldts sjukdom
  • Jakob
  • morbus Creutzfeldt-Jakob
  • sporadinen CJD
  • subakut spongioform encefalopati
  • syndroma Creutzfeldt-Jakob
  • Swedish

URI

http://www.yso.fi/onto/mesh/D007562

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