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Concept information

Preferred term

Prion Diseases  

Type

  • Topical Descriptor

Entry terms

  • Dementias, Transmissible
  • Dementia, Transmissible
  • Disorder, Prion-Induced
  • Disorders, Prion-Induced
  • Encephalopathies, Spongiform, Transmissible
  • Encephalopathies, Transmissible Spongiform
  • Encephalopathy, Transmissible Spongiform
  • Prion-Associated Disorders
  • Prion Disease
  • Prion Induced Disorder
  • Prion-Induced Disorder
  • Prion-Induced Disorders
  • Prion Protein Disease
  • Prion Protein Diseases
  • Spongiform Encephalopathies, Transmissible
  • Spongiform Encephalopathy, Transmissible
  • Transmissible Dementia
  • Transmissible Dementias
  • Transmissible Spongiform Encephalopathies
  • Transmissible Spongiform Encephalopathy

Note

  • general or unspecified; prefer specifics

Scope note

  • A group of genetic, infectious, or sporadic degenerative human and animal nervous system disorders associated with abnormal PRIONS. These diseases are characterized by conversion of the normal prion protein to an abnormal configuration via a post-translational process. In humans, these conditions generally feature DEMENTIA; ATAXIA; and a fatal outcome. Pathologic features include a spongiform encephalopathy without evidence of inflammation. The older literature occasionally refers to these as unconventional SLOW VIRUS DISEASES. (From Proc Natl Acad Sci USA 1998 Nov 10;95(23):13363-83)

History note

  • 1993

In other languages

URI

http://www.yso.fi/onto/mesh/D017096

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