Concept information
Preferred term
Immunoglobulin Light-chain Amyloidosis
Type
-
Topical Descriptor
Entry terms
- AL Amyloidoses
- AL Amyloidosis
- Amyloidoses, Primary
- Amyloidoses, Primary Systemic
- Amyloidosis, Immunoglobulin Light chain
- Amyloidosis, Immunoglobulin Light-chain
- Amyloidosis, Primary
- Amyloidosis, Primary Systemic
- Monoclonal Immunoglobulin Deposition Disease
- Primary Amyloidoses
- Primary Amyloidosis
- Primary Systemic Amyloidoses
- Primary Systemic Amyloidosis
- Systemic Amyloidoses, Primary
- Systemic Amyloidosis, Primary
Scope note
- A nonproliferative disorder of PLASMA CELLS characterized by excessive production and misfolding of IMMUNOGLOBULIN LIGHT CHAINS that form insoluble amyloid fibrils (see AMYLOID DEPOSITS) in various tissues. Clinical features include LIVER FAILURE; MULTIPLE MYELOMA; NEPHROTIC SYNDROME; RESTRICTIVE CARDIOMYOPATHY, and neuropathies.
History note
- 2018(2010)
In other languages
-
Finnish
-
Swedish
-
Primär amyloidos
-
Primär systemisk amyloidos
URI
http://www.yso.fi/onto/mesh/D000075363
{{label}}
{{#each values }} {{! loop through ConceptPropertyValue objects }}
{{#if prefLabel }}
{{/if}}
{{/each}}
{{#if notation }}{{ notation }} {{/if}}{{ prefLabel }}
{{#ifDifferentLabelLang lang }} ({{ lang }}){{/ifDifferentLabelLang}}
{{#if vocabName }}
{{ vocabName }}
{{/if}}