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Concept information

Preferred term

Hamman-Rich Syndrome  

Type

  • Topical Descriptor

Entry terms

  • Acute Interstitial Pneumonia
  • Acute Interstitial Pneumonias
  • Acute Interstitial Pneumonitides
  • Acute Interstitial Pneumonitis
  • Hamman Rich Disease
  • Hamman-Rich Disease
  • Interstitial Pneumonia, Acute
  • Interstitial Pneumonitis, Acute
  • Pneumonia, Acute Interstitial
  • Pneumonitis, Acute Interstitial

Scope note

  • Acute idiopathic interstitial pneumonitis characterized by diffuse PULMONARY ALVEOLI damage with uniform edematous connective tissue proliferation. It is often associated with extensive fibroblastic distortion of the lung parenchyma and leads to ADULT RESPIRATORY DISTRESS SYNDROME in later stages.

History note

  • 2020; for HAMMAN-RICH SYNDROME use PULMONARY FIBROSIS 1984-2019; for HAMMAN-RICH SYNDROME use IDIOPATHIC PULMONARY FIBROSIS 2010-2019

In other languages

URI

http://www.yso.fi/onto/mesh/D000080203

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