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Enzymes and Coenzymes > Enzymes > Multifunctional Enzymes > Acetyl-CoA Carboxylase > Propionyl-Coenzyme A Carboxylase
... > Enzymes and Coenzymes > Enzymes > Ligases > Carbon-Carbon Ligases > Acetyl-CoA Carboxylase > Propionyl-Coenzyme A Carboxylase

Preferred term

Propionyl-Coenzyme A Carboxylase  

Type

  • Topical Descriptor

Broader concept

Entry terms

  • Propionyl CoA Carboxylase
  • Propionyl-CoA Carboxylase

Scope note

  • Mitochondrial carboxylase that is involved in the catabolism of odd chain fatty acids and branched amino acids. Dysfunction of propionyl-CoA carboxylase leads to the inherited metabolic disorder PROPIONIC ACIDEMIA. In bacteria it is an ATP-dependent carboxylase in CO2 fixation reactions where propionyl-CoA is converted to (S)-methylmalonyl-CoA.

History note

  • 2024; use Methylmalonyl-CoA Decarboxylase 2004-2023

In other languages

URI

http://www.yso.fi/onto/mesh/D000095562

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RDF/XML TURTLE JSON-LD Created 7/26/23, last modified 2/26/23