Concept information
Preferred term
Cerebroside-Sulfatase
Type
-
Topical Descriptor
Broader concept
Entry terms
- Arylsulfatase A
- Sulfatase, Sulfatidate
- Sulfatidate Sulfatase
Note
- /defic: consider also LEUKODYSTROPHY, METACHROMATIC
Scope note
- An enzyme that catalyzes the hydrolysis of cerebroside 3-sulfate (sulfatide) to yield a cerebroside and inorganic sulfate. A marked deficiency of arylsulfatase A, which is considered the heat-labile component of cerebroside sulfatase, has been demonstrated in all forms of metachromatic leukodystrophy (LEUKODYSTROPHY, METACHROMATIC). EC 3.1.6.8.
History note
- 87(76); was see under SULFATASES 1976-86
In other languages
-
Finnish
-
Swedish
URI
http://www.yso.fi/onto/mesh/D002553
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