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Concept information

Preferred term

Dermatomyositis  

Type

  • Topical Descriptor

Entry terms

  • Dermatopolymyositis
  • Polymyositis Dermatomyositis
  • Polymyositis-Dermatomyositis

Note

  • coordinate with PARANEOPLASTIC SYNDROMES if pertinent

Scope note

  • A subacute or chronic inflammatory disease of muscle and skin, marked by proximal muscle weakness and a characteristic skin rash. The illness occurs with approximately equal frequency in children and adults. The skin lesions usually take the form of a purplish rash (or less often an exfoliative dermatitis) involving the nose, cheeks, forehead, upper trunk, and arms. The disease is associated with a complement mediated intramuscular microangiopathy, leading to loss of capillaries, muscle ischemia, muscle-fiber necrosis, and perifascicular atrophy. The childhood form of this disease tends to evolve into a systemic vasculitis. Dermatomyositis may occur in association with malignant neoplasms. (From Adams et al., Principles of Neurology, 6th ed, pp1405-6)

In other languages

  • Finnish

  • dermatomyosiitit
  • dermatomyositis non specificata
  • dermatopolymyosiitti
  • dermatopolymyositis
  • dermatopolymyositis non specificata
  • iho- ja lihastulehdukset
  • iho- ja lihastulehdus
  • määrittämätön dermatomyosiitti
  • määrittämätön dermatopolymyosiitti
  • polymyosiitti
  • polymyosiitti-dermatomyosiitit
  • polymyosiitti-dermatomyosiitti
  • reumaattinen lihastulehdus
  • Swedish

URI

http://www.yso.fi/onto/mesh/D003882

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