Concept information
Preferred term
Hemoglobinuria, Paroxysmal
Type
-
Topical Descriptor
Broader concept
Entry terms
- Paroxysmal Hemoglobinuria
Scope note
- A condition characterized by the recurrence of HEMOGLOBINURIA caused by intravascular HEMOLYSIS. In cases occurring upon cold exposure (paroxysmal cold hemoglobinuria), usually after infections, there is a circulating antibody which is also a cold hemolysin. In cases occurring during or after sleep (paroxysmal nocturnal hemoglobinuria), the clonal hematopoietic stem cells exhibit a global deficiency of cell membrane proteins.
History note
- 78; was MARCHIAFAVA-MICHELI SYNDROME 1963-77
In other languages
-
Finnish
-
haemoglobinuria nocturna
-
haemoglobinuria paroxysmalis nocturna
-
kohtauksittainen hemoglobiinivirtsaisuus
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kohtauksittainen verenpunavirtsaisuus
-
kohtauksittainen yöllinen hemoglobiinivirtsaisuus
-
kohtauksittainen yöllinen verenpunavirtsaisuus
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Marchiafava
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Marchiafava-Micheli
-
Marchiafava-Michelin tauti
-
Marchiafavan tauti
-
paroksysmaalinen nokturnaalinen hemoglobinuria
-
paroxysmal nattlig hemoglobinuri (Marchiafava-Micheli)
-
PNH
-
Swedish
URI
http://www.yso.fi/onto/mesh/D006457
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