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Concept information

Preferred term

Hirschsprung Disease  

Type

  • Topical Descriptor

Entry terms

  • Aganglionic Megacolon
  • Congenital Megacolon
  • Disease, Hirschsprung's
  • Hirschsprung's Disease
  • Hirschsprungs Disease
  • Megacolon, Aganglionic
  • Megacolon, Congenital

Note

  • acquired megacolon = MEGACOLON

Scope note

  • Congenital MEGACOLON resulting from the absence of ganglion cells (aganglionosis) in a distal segment of the LARGE INTESTINE. The aganglionic segment is permanently contracted thus causing dilatation proximal to it. In most cases, the aganglionic segment is within the RECTUM and SIGMOID COLON.

History note

  • 83; was HIRSCHSPRUNG'S DISEASE see MEGACOLON 1963-82

In other languages

  • Finnish

  • aganglionosis colonica totalis
  • aganglionosis intestinalis totalis
  • Hirschprung
  • Hirschprungin tauti
  • Hirschsprung
  • Hirschsprungin tauti lyhyessä suolen osassa
  • Hirschsprungin tauti pitkässä suolen osassa
  • koolonin täydellinen aganglionoosi
  • megacolon congenitum
  • megacolon congenitum aganglionicum
  • morbus Hirschsprung
  • morbus Hirschsprung segmenti intestinalis brevis
  • morbus Hirschsprung segmenti intestinalis longi
  • muu suolen aganglionoosi
  • suolen aganglionoosi
  • suolen täydellinen aganglionoosi
  • synnynnäinen aganglioninen megakoolon
  • synnynnäinen jättikoolon
  • Swedish

  • Medfödd megakolon

URI

http://www.yso.fi/onto/mesh/D006627

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