Concept information
Immune System Diseases
Immunoproliferative Disorders
Lymphoproliferative Disorders
Heavy Chain Disease
Preferred term
Immunoproliferative Small Intestinal Disease
Type
-
Topical Descriptor
Broader concept
Entry terms
- alpha Chain Disease
- alpha-Chain Disease
- alpha-Chain Diseases
- Disease, alpha-Chain
- Diseases, alpha-Chain
- Heavy Chain Disease, IgA Type
- IPSID
- Lymphoma, Mediterranean
- Mediterranean Lymphoma
Scope note
- A condition that is caused by HYPERPLASIA of LYMPHOCYTES in the small intestine (INTESTINE, SMALL) and the mesenteric LYMPH NODES. These lymphocytes produce an anomalous alpha heavy chain protein. Generally, these IPSID patients have either concurrent LYMPHOMA or develop lymphoma within a few years. The disease was first described in the Mediterranean region and is characterized by malabsorption; WEIGHT LOSS; DIARRHEA; and STEATORRHEA.
History note
- 87
In other languages
-
Finnish
-
immunoproliferatiivinen ohutsuolen tauti
-
immunoproliferativ tunntarmssjukdom
-
lymphoma mediterraneum
-
medelhavslymfom
-
morbus intestini tenuis immunoproliferativus
-
välimeren lymfooma
-
Swedish
URI
http://www.yso.fi/onto/mesh/D007161
{{label}}
{{#each values }} {{! loop through ConceptPropertyValue objects }}
{{#if prefLabel }}
{{/if}}
{{/each}}
{{#if notation }}{{ notation }} {{/if}}{{ prefLabel }}
{{#ifDifferentLabelLang lang }} ({{ lang }}){{/ifDifferentLabelLang}}
{{#if vocabName }}
{{ vocabName }}
{{/if}}