Concept information
Preferred term
Creutzfeldt-Jakob Syndrome
Type
-
Topical Descriptor
Broader concept
Entry terms
- CJD (Creutzfeldt Jakob Disease)
- CJD (Creutzfeldt-Jakob Disease)
- Creutzfeldt Jacob Disease
- Creutzfeldt Jakob Disease
- Creutzfeldt-Jakob Disease
- Disease, Creutzfeldt Jacob
- Disease, Creutzfeldt-Jakob
- Disease, Jakob-Creutzfeldt
- Encephalopathies, Subacute Spongiform
- Encephalopathy, Subacute Spongiform
- Jacob Disease, Creutzfeldt
- Jakob Creutzfeldt Disease
- Jakob-Creutzfeldt Disease
- Jakob Creutzfeldt Syndrome
- Jakob-Creutzfeldt Syndrome
- Spongiform Encephalopathies, Subacute
- Spongiform Encephalopathy, Subacute
- Subacute Spongiform Encephalopathies
- Subacute Spongiform Encephalopathy
- Syndrome, Jakob-Creutzfeldt
Scope note
- A rare transmissible encephalopathy most prevalent between the ages of 50 and 70 years. Affected individuals may present with sleep disturbances, personality changes, ATAXIA; APHASIA, visual loss, weakness, muscle atrophy, MYOCLONUS, progressive dementia, and death within one year of disease onset. A familial form exhibiting autosomal dominant inheritance and a new variant CJD (potentially associated with ENCEPHALOPATHY, BOVINE SPONGIFORM) have been described. Pathological features include prominent cerebellar and cerebral cortical spongiform degeneration and the presence of PRIONS. (From N Engl J Med, 1998 Dec 31;339(27))
History note
- 1991; use JAKOB-CREUTZFELDT SYNDROME 1981-1990, use CREUTZFELDT-JAKOB DISEASE 1969-1980
In other languages
-
Finnish
-
CJD
-
Creutzfeld-Jakob disease
-
Creutzfeldt
-
Creutzfeldt-Jakob
-
Creutzfeldt-Jakobin oireyhtymä
-
Creutzfeldt-Jakobin syndrooma
-
encephalopathia spongiformis subacuta
-
Jacob-Creutzfeldts sjukdom
-
Jakob
-
morbus Creutzfeldt-Jakob
-
sporadinen CJD
-
subakut spongioform encefalopati
-
syndroma Creutzfeldt-Jakob
-
Swedish
URI
http://www.yso.fi/onto/mesh/D007562
{{label}}
{{#each values }} {{! loop through ConceptPropertyValue objects }}
{{#if prefLabel }}
{{/if}}
{{/each}}
{{#if notation }}{{ notation }} {{/if}}{{ prefLabel }}
{{#ifDifferentLabelLang lang }} ({{ lang }}){{/ifDifferentLabelLang}}
{{#if vocabName }}
{{ vocabName }}
{{/if}}