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Concept information

Preferred term

Medullary Sponge Kidney  

Type

  • Topical Descriptor

Broader concept

Entry terms

  • Cacchi Ricci Disease
  • Cacchi Ricci Syndrome
  • Cacchi-Ricci Syndrome
  • Canalicular Ectasia, Precalyceal
  • Canalicular Ectasias, Precalyceal
  • Disease, Cacchi Ricci
  • Ectasia, Precalyceal Canalicular
  • Ectasias, Precalyceal Canalicular
  • Kidney, Sponge
  • Kidneys, Sponge
  • Precalyceal Canalicular Ectasia
  • Precalyceal Canalicular Ectasias
  • Ricci Disease, Cacchi
  • Sponge Kidney
  • Sponge Kidneys
  • Syndrome, Cacchi-Ricci

Scope note

  • A non-hereditary KIDNEY disorder characterized by the abnormally dilated (ECTASIA) medullary and inner papillary portions of the collecting ducts. These collecting ducts usually contain CYSTS or DIVERTICULA filled with jelly-like material or small calculi (KIDNEY STONES) leading to infections or obstruction. It should be distinguished from congenital or hereditary POLYCYSTIC KIDNEY DISEASES.

History note

  • 2006 (1965)

In other languages

URI

http://www.yso.fi/onto/mesh/D007691

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