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Preferred term

Multiple Endocrine Neoplasia  

Type

  • Topical Descriptor

Entry terms

  • Adenomatoses, Familial Endocrine
  • Adenomatoses, Multiple Endocrine
  • Adenomatosis, Familial Endocrine
  • Adenomatosis, Multiple Endocrine
  • Adenopathies, Multiple Endocrine
  • Adenopathy, Multiple Endocrine
  • Endocrine Adenomatoses, Familial
  • Endocrine Adenomatoses, Multiple
  • Endocrine Adenomatosis, Familial
  • Endocrine Adenomatosis, Multiple
  • Endocrine Adenopathies, Multiple
  • Endocrine Adenopathy, Multiple
  • Endocrine Neoplasia, Multiple
  • Endocrine Neoplasms, Multiple
  • Familial Endocrine Adenomatoses
  • Familial Endocrine Adenomatosis
  • Multiple Endocrine Adenomatoses
  • Multiple Endocrine Adenomatosis
  • Multiple Endocrine Adenopathies
  • Multiple Endocrine Adenopathy
  • Multiple Endocrine Neoplasia Syndrome
  • Multiple Endocrine Neoplasia Syndromes
  • Multiple Endocrine Neoplasms
  • Neoplasia, Multiple Endocrine
  • Neoplasms, Multiple Endocrine

Note

  • general or unspecified; prefer specifics; coordinate IM with specific endocrine/neoplasm pre-coordinates (IM) + specific histological type (IM) if pertinent

Scope note

  • A group of autosomal dominant diseases characterized by the combined occurrence of tumors involving two or more ENDOCRINE GLANDS that secrete PEPTIDE HORMONES or AMINES. These neoplasias are often benign but can be malignant. They are classified by the endocrine glands involved and the degree of aggressiveness. The two major forms are MEN1 and MEN2 with gene mutations on CHROMOSOME 11 and CHROMOSOME 10, respectively.

History note

  • 95; was NEOPLASMS, MULTIPLE ENDOCRINE 1983-94; was ADENOMATOSIS, FAMILIAL ENDOCRINE 1965-82 (Prov 1964)

In other languages

URI

http://www.yso.fi/onto/mesh/D009377

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