Concept information
Preferred term
Neoplastic Syndromes, Hereditary
Type
-
Topical Descriptor
Broader concept
Narrower concepts
- Adenomatous Polyposis Coli
- Basal Cell Nevus Syndrome
- Birt-Hogg-Dube Syndrome
- Colorectal Neoplasms, Hereditary Nonpolyposis
- Dysplastic Nevus Syndrome
- Exostoses, Multiple Hereditary
- Hamartoma Syndrome, Multiple
- Hereditary Breast and Ovarian Cancer Syndrome
- Li-Fraumeni Syndrome
- Multiple Endocrine Neoplasia
- Neurofibromatoses
- Peutz-Jeghers Syndrome
- Tuberous Sclerosis
- Wilms Tumor
Entry terms
- Cancer Syndrome, Hereditary
- Cancer Syndromes, Hereditary
- Hereditary Cancer Syndrome
- Hereditary Cancer Syndromes
- Hereditary Neoplastic Syndrome
- Hereditary Neoplastic Syndromes
- Neoplastic Syndrome, Hereditary
- Syndrome, Hereditary Cancer
- Syndrome, Hereditary Neoplastic
- Syndromes, Hereditary Cancer
- Syndromes, Hereditary Neoplastic
Note
- coordinate with specific hereditary organ/neoplasm term or specific hereditary histological type
Scope note
- The condition of a pattern of malignancies within a family, but not every individual's necessarily having the same neoplasm. Characteristically the tumor tends to occur at an earlier than average age, individuals may have more than one primary tumor, the tumors may be multicentric, usually more than 25 percent of the individuals in direct lineal descent from the proband are affected, and the cancer predisposition in these families behaves as an autosomal dominant trait with about 60 percent penetrance.
History note
- 87
In other languages
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Finnish
-
hereditaariset neoplastiset oireyhtymät
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hereditaariset neoplastiset syndroomat
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hereditääriset neoplastiset oireyhtymät
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hereditääriset neoplastiset syndroomat
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perinnölliset neoplastiset syndroomat
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periytyvät neoplastiset oireyhtymät
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periytyvät neoplastiset syndroomat
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Swedish
-
Cancer syndrom, ärftliga
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Neoplastiska syndrom, ärftliga
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Ärftliga cancer syndrom
URI
http://www.yso.fi/onto/mesh/D009386
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