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Congenital, Hereditary, and Neonatal Diseases and Abnormalities > Genetic Diseases, Inborn > Heredodegenerative Disorders, Nervous System > Spinocerebellar Degenerations > Olivopontocerebellar Atrophies
Nervous System Diseases > Neurodegenerative Diseases > Heredodegenerative Disorders, Nervous System > Spinocerebellar Degenerations > Olivopontocerebellar Atrophies
Nervous System Diseases > Central Nervous System Diseases > Spinal Cord Diseases > Spinocerebellar Degenerations > Olivopontocerebellar Atrophies
... > Nervous System Diseases > Central Nervous System Diseases > Brain Diseases > Cerebellar Diseases > Spinocerebellar Degenerations > Olivopontocerebellar Atrophies
Nervous System Diseases > Central Nervous System Diseases > Movement Disorders > Multiple System Atrophy > Olivopontocerebellar Atrophies
... > Nervous System Diseases > Central Nervous System Diseases > Brain Diseases > Basal Ganglia Diseases > Multiple System Atrophy > Olivopontocerebellar Atrophies
Nervous System Diseases > Autonomic Nervous System Diseases > Primary Dysautonomias > Multiple System Atrophy > Olivopontocerebellar Atrophies
Nervous System Diseases > Neurodegenerative Diseases > Synucleinopathies > Multiple System Atrophy > Olivopontocerebellar Atrophies
... > Nutritional and Metabolic Diseases > Metabolic Diseases > Proteostasis Deficiencies > Synucleinopathies > Multiple System Atrophy > Olivopontocerebellar Atrophies

Preferred term

Olivopontocerebellar Atrophies  

Type

  • Topical Descriptor

Broader concept

Related concepts

Entry terms

  • Ataxia, Presenile
  • Atrophy, Olivo-Ponto-Cerebellar
  • Atrophy, Pontoolivocerebellar
  • Degeneration, Olivo-Ponto-Cerebellar
  • Degeneration, Olivopontocerebellar
  • Dejerine Thomas Syndrome
  • Dejerine-Thomas Syndrome
  • Olivo Ponto Cerebellar Atrophy
  • Olivo-Ponto-Cerebellar Atrophy
  • Olivopontocerebellar Atrophy
  • Olivo Ponto Cerebellar Degeneration
  • Olivo-Ponto-Cerebellar Degeneration
  • Olivopontocerebellar Degeneration
  • Olivo-Ponto-Cerebellar Degenerations
  • Olivopontocerebellar Degenerations
  • Pontoolivocerebellar Atrophies
  • Pontoolivocerebellar Atrophy
  • Presenile Ataxia
  • Presenile Ataxias
  • Syndrome, Dejerine-Thomas

Scope note

  • A group of inherited and sporadic disorders which share progressive ataxia in combination with atrophy of the CEREBELLUM; PONS; and inferior olivary nuclei. Additional clinical features may include MUSCLE RIGIDITY; NYSTAGMUS, PATHOLOGIC; RETINAL DEGENERATION; MUSCLE SPASTICITY; DEMENTIA; URINARY INCONTINENCE; and OPHTHALMOPLEGIA. The familial form has an earlier onset (second decade) and may feature spinal cord atrophy. The sporadic form tends to present in the fifth or sixth decade, and is considered a clinical subtype of MULTIPLE SYSTEM ATROPHY. (From Adams et al., Principles of Neurology, 6th ed, p1085)

History note

  • 2000(1987)

In other languages

  • olivopontoserebellaariset degeneraatiot

    Finnish

  • atrophia olivopontocerebellaris
  • degeneratio olivopontocerebellaris
  • olivopontoserebellaarinen atrofia
  • olivopontoserebellaarinen degeneraatio
  • olivopontoserebellaariset atrofiat
  • Olivopontocerebellär atrofi

    Swedish

  • Dejerine-Thomas syndrom
  • Olivopontocerebellär degeneration
  • Presenil ataxi

URI

http://www.yso.fi/onto/mesh/D009849

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