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Concept information

Preferred term

Spinocerebellar Degenerations  

Type

  • Topical Descriptor

Entry terms

  • Degeneration, Spino Cerebellar
  • Degeneration, Spino-Cerebellar
  • Degenerations, Spino Cerebellar
  • Spino Cerebellar Degeneration
  • Spino-Cerebellar Degeneration
  • Spinocerebellar Degeneration
  • Spino Cerebellar Degenerations
  • Spino-Cerebellar Degenerations
  • Spinocerebellar Disease
  • Spinocerebellar Diseases

Scope note

  • A heterogenous group of degenerative syndromes marked by progressive cerebellar dysfunction either in isolation or combined with other neurologic manifestations. Sporadic and inherited subtypes occur. Inheritance patterns include autosomal dominant, autosomal recessive, and X-linked.

History note

  • 2000(1987)

In other languages

  • Finnish

  • selkäydin-pikkuaivorappeuma
  • selkäydin-pikkuaivorappeumat
  • spinoserebellaarinen degeneraatio
  • spinoserebellaarinen rappeuma
  • spinoserebellaariset degeneraatiot
  • Swedish

  • Cerebellär ataxi med sen debut
  • Cerebellär ataxi med tidig debut
  • Hereditär ataxi
  • Marinesco-Sjögrens syndrom
  • Spinocerebellära sjukdomar
  • Ärftlig ataxi

URI

http://www.yso.fi/onto/mesh/D013132

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