Concept information
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Central Nervous System Diseases
Central Nervous System Infections
Infectious Encephalitis
Encephalitis, Viral
Preferred term
Subacute Sclerosing Panencephalitis
Type
-
Topical Descriptor
Broader concept
Entry terms
- Encephalitis, Inclusion Body, Measles
- Inclusion Body Encephalitis, Measles
- Leukoencephalitides, Subacute Sclerosing
- Leukoencephalitis, Subacute Sclerosing
- Leukoencephalitis, Van Bogaert
- Leukoencephalitis, Van Bogaert's
- Leukoencephalitis, Van Bogaerts
- Measles Inclusion Body Encephalitis
- Panencephalitis, Subacute Sclerosing
- Sclerosing Leukoencephalitides, Subacute
- Sclerosing Leukoencephalitis, Subacute
- Sclerosing Panencephalitis, Subacute
- SSPE
- Subacute Sclerosing Leukoencephalitides
- Subacute Sclerosing Leukoencephalitis
- Van Bogaert Leukoencephalitis
- Van Bogaert's Leukoencephalitis
- Van Bogaerts Leukoencephalitis
Scope note
- A rare, slowly progressive encephalitis caused by chronic infection with the MEASLES VIRUS. The condition occurs primarily in children and young adults, approximately 2-8 years after the initial infection. A gradual decline in intellectual abilities and behavioral alterations are followed by progressive MYOCLONUS; MUSCLE SPASTICITY; SEIZURES; DEMENTIA; autonomic dysfunction; and ATAXIA. DEATH usually occurs 1-3 years after disease onset. Pathologic features include perivascular cuffing, eosinophilic cytoplasmic inclusions, neurophagia, and fibrous gliosis. It is caused by the SSPE virus, which is a defective variant of MEASLES VIRUS. (From Adams et al., Principles of Neurology, 6th ed, pp767-8)
History note
- 71; VAN BOGAERT'S LEUKOENCEPHALITIS was see under SUBACUTE SCLEROSING PANENCEPHALITIS 1971-78; was see under CEREBRAL SCLEROSIS, DIFFUSE 1963-70
In other languages
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Finnish
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Dawson
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Dawsonin inkluusiokappale -aivotulehdus
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Dawsons inclusion body-encefalit
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encephalitis cum corporibus inclusionis Dawson
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leucoencephalopathia sclerosificans Van Bogaert
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panencephalitis sclerosans subacuta
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panencephalitis sclerosificans subacuta
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SSPE
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subakut skleroserande panencefalit [SSPE]
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van Bogaert
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van Bogaertin sklerosoiva leukoenkefalopatia
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van Bogaerts skleroserande leukoencefalopati
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Swedish
URI
http://www.yso.fi/onto/mesh/D013344
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