Concept information
Infections
Central Nervous System Infections
Central Nervous System Viral Diseases
Encephalitis, Viral
...
Central Nervous System Diseases
Central Nervous System Infections
Central Nervous System Viral Diseases
Encephalitis, Viral
Preferred term
Subacute Sclerosing Panencephalitis
Type
-
Topical Descriptor
Broader concept
Entry terms
- Encephalitis, Inclusion Body, Measles
- Inclusion Body Encephalitis, Measles
- Leukoencephalitides, Subacute Sclerosing
- Leukoencephalitis, Subacute Sclerosing
- Leukoencephalitis, Van Bogaert
- Leukoencephalitis, Van Bogaert's
- Leukoencephalitis, Van Bogaerts
- Measles Inclusion Body Encephalitis
- Panencephalitis, Subacute Sclerosing
- Sclerosing Leukoencephalitides, Subacute
- Sclerosing Leukoencephalitis, Subacute
- Sclerosing Panencephalitis, Subacute
- SSPE
- Subacute Sclerosing Leukoencephalitides
- Subacute Sclerosing Leukoencephalitis
- Van Bogaert Leukoencephalitis
- Van Bogaert's Leukoencephalitis
- Van Bogaerts Leukoencephalitis
Scope note
- A rare, slowly progressive encephalitis caused by chronic infection with the MEASLES VIRUS. The condition occurs primarily in children and young adults, approximately 2-8 years after the initial infection. A gradual decline in intellectual abilities and behavioral alterations are followed by progressive MYOCLONUS; MUSCLE SPASTICITY; SEIZURES; DEMENTIA; autonomic dysfunction; and ATAXIA. DEATH usually occurs 1-3 years after disease onset. Pathologic features include perivascular cuffing, eosinophilic cytoplasmic inclusions, neurophagia, and fibrous gliosis. It is caused by the SSPE virus, which is a defective variant of MEASLES VIRUS. (From Adams et al., Principles of Neurology, 6th ed, pp767-8)
History note
- 71; VAN BOGAERT'S LEUKOENCEPHALITIS was see under SUBACUTE SCLEROSING PANENCEPHALITIS 1971-78; was see under CEREBRAL SCLEROSIS, DIFFUSE 1963-70
In other languages
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Finnish
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Dawson
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Dawsonin inkluusiokappale -aivotulehdus
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Dawsons inclusion body-encefalit
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encephalitis cum corporibus inclusionis Dawson
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leucoencephalopathia sclerosificans Van Bogaert
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panencephalitis sclerosans subacuta
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panencephalitis sclerosificans subacuta
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SSPE
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subakut skleroserande panencefalit [SSPE]
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van Bogaert
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van Bogaertin sklerosoiva leukoenkefalopatia
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van Bogaerts skleroserande leukoencefalopati
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Swedish
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SSPE
URI
http://www.yso.fi/onto/mesh/D013344
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