Skip to main content

Search from vocabulary

Content language

Concept information

Preferred term

POEMS Syndrome  

Type

  • Topical Descriptor

Entry terms

  • Crow Fukase Syndrome
  • Crow-Fukase Syndrome
  • Organomegalies, Polyneuropathy
  • Organomegaly, Polyneuropathy
  • Polyneuropathy Organomegalies
  • Polyneuropathy Organomegaly
  • Polyneuropathy, Organomegaly, Endocrinopathy, M Protein, and Skin Changes Syndrome
  • Syndrome, Crow-Fukase
  • Syndrome, Takatsuki's
  • Takatsuki's Syndrome
  • Takatsuki Syndrome

Scope note

  • A multisystemic disorder characterized by a sensorimotor polyneuropathy (POLYNEUROPATHIES), organomegaly, endocrinopathy, monoclonal gammopathy, and pigmentary skin changes. Other clinical features which may be present include EDEMA; CACHEXIA; microangiopathic glomerulopathy; pulmonary hypertension (HYPERTENSION, PULMONARY); cutaneous necrosis; THROMBOCYTOSIS; and POLYCYTHEMIA. This disorder is frequently associated with osteosclerotic myeloma. (From Adams et al., Principles of Neurology, 6th ed, p1335; Rev Med Interne 1997;18(7):553-62)

History note

  • 1992

In other languages

URI

http://www.yso.fi/onto/mesh/D016878

Download this concept:

RDF/XML TURTLE JSON-LD Created 5/2/91, last modified 6/25/10