Concept information
Preferred term
Dermatofibrosarcoma
Type
-
Topical Descriptor
Broader concept
Entry terms
- Darier Ferrand Tumor
- Darier-Ferrand Tumor
- Darier Hoffmann Tumor
- Darier-Hoffmann Tumor
- Dermatofibrosarcoma Protuberan
- Dermatofibrosarcoma Protuberans
- Protuberan, Dermatofibrosarcoma
- Protuberans, Dermatofibrosarcoma
- Tumor, Darier-Ferrand
- Tumor, Darier-Hoffmann
Note
- coordinate with with SKIN NEOPLASMS
Scope note
- A sarcoma of the deep layers of the skin. The tumors are locally aggressive tends to recur but rarely metastatic. It can be classified into variants depending on the cell type tumors are derived from or by its characteristics: Pigmented variant from MELANIN-containing DERMAL DENDRITIC CELLS; Myxoid variant, myxoid STROMAL CELLS; Giant cell variant characterized by GIANT CELLS in the tumors; and Fibrosarcomatous variant chracterized by tumor areas histologically indistinguishable from FIBROSARCOMA.
History note
- 94
In other languages
-
Finnish
-
dermatofibrosarcoma
-
Swedish
URI
http://www.yso.fi/onto/mesh/D018223
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