Concept information
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Peripheral Nervous System Diseases
Peripheral Nervous System Neoplasms
Nerve Sheath Neoplasms
Neurofibroma
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Nervous System Neoplasms
Peripheral Nervous System Neoplasms
Nerve Sheath Neoplasms
Neurofibroma
Preferred term
Neurofibroma, Plexiform
Type
-
Topical Descriptor
Broader concept
Entry terms
- Elephantiasis Neuromatoses
- Elephantiasis Neuromatosis
- Neuroma, Plexiform
- Neuromas, Plexiform
- Pachydermatocele
- Pachydermatoceles
- Plexiform Neuroma
- Plexiform Neuromas
- Tumor Royale
Note
- coord IM with precoord organ/neopl term (IM)
Scope note
- A type of neurofibroma manifesting as a diffuse overgrowth of subcutaneous tissue, usually involving the face, scalp, neck, and chest but occasionally occurring in the abdomen or pelvis. The tumors tend to progress, and may extend along nerve roots to eventually involve the spinal roots and spinal cord. This process is almost always a manifestation of NEUROFIBROMATOSIS 1. (From Adams et al., Principles of Neurology, 6th ed, p1016; J Pediatr 1997 Nov;131(5):678-82)
History note
- 94
In other languages
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Finnish
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Swedish
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Elephantiasis neuromatosis
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Neurom, plexiform
URI
http://www.yso.fi/onto/mesh/D018318
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