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Concept information

Preferred term

Hypokalemic Periodic Paralysis  

Type

  • Topical Descriptor

Entry terms

  • Familial Hypokalemic Periodic Paralysis
  • HOKPP
  • Hypokalemic Periodic Paralysis, Familial
  • HYPOKPP
  • HYPOPP
  • Paralysis, Hypokalemic Periodic
  • Periodic Paralysis Hypokalemic
  • Periodic Paralysis- Hypokalemic
  • Periodic Paralysis- Hypokalemics
  • Primary Hypokalemic Periodic Paralysis
  • Westphall Disease

Scope note

  • An autosomal dominant familial disorder characterized by recurrent episodes of skeletal muscle weakness associated with falls in serum potassium levels. The condition usually presents in the first or second decade of life with attacks of trunk and leg paresis during sleep or shortly after awakening. Symptoms may persist for hours to days and generally are precipitated by exercise or a meal high in carbohydrates. (Adams et al., Principles of Neurology, 6th ed, p1483)

History note

  • 2000

In other languages

  • Finnish

  • familiaalinen hypokaleeminen kohtauksittainen halvaus
  • familiaalinen hypokaleeminen periodinen paralyysi
  • hypokaleeminen kohtauksittainen halvaus
  • hypokaleeminen periodinen paralyysi
  • paralysis periodica
  • primaarinen hypokaleeminen kohtauksittainen halvaus
  • primaarinen hypokaleeminen periodinen paralyysi
  • suvuittainen hypokaleeminen periodinen paralyysi
  • suvuittainen hypokaleminen kohtauksittainen halvaus
  • Swedish

  • Familjär hypokalemisk periodisk paralys

URI

http://www.yso.fi/onto/mesh/D020514

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