Concept information
Preferred term
Isovaleryl-CoA Dehydrogenase
Type
-
Topical Descriptor
Broader concept
Entry terms
- CoA Dehydrogenase, Isovaleryl
- Dehydrogenase, Isovaleryl CoA
- Dehydrogenase, Isovaleryl-Coenzyme A
- Isovaleryl CoA Dehydrogenase
- Isovaleryl Coenzyme A Dehydrogenase
- Isovaleryl-Coenzyme A Dehydrogenase
Scope note
- A mitochondrial flavoprotein, this enzyme catalyzes the oxidation of 3-methylbutanoyl-CoA to 3-methylbut-2-enoyl-CoA using FAD as a cofactor. Defects in the enzyme, is associated with isovaleric acidemia (IVA).
History note
- 2006(1973)
In other languages
-
Finnish
-
Swedish
URI
http://www.yso.fi/onto/mesh/D050769
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