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Concept information

Preferred term

1-Pyrroline-5-Carboxylate Dehydrogenase  

Type

  • Topical Descriptor

Entry terms

  • Dehydrogenase, GGS
  • Dehydrogenase, Glutamic-Gamma-Semialdehyde
  • Dehydrogenase, Glutamyl-Gamma-Semialdehyde
  • Delta(1)-Pyrroline-5-Carboxylate Dehydrogenase
  • GGS Dehydrogenase
  • Glutamic Gamma Semialdehyde Dehydrogenase
  • Glutamic-Gamma-Semialdehyde Dehydrogenase
  • Glutamyl Gamma Semialdehyde Dehydrogenase
  • Glutamyl-Gamma-Semialdehyde Dehydrogenase
  • NADP+ Specific 8 Glutamate Semialdehyde Dehydrogenase
  • NADP+ Specific 8-Glutamate Semialdehyde Dehydrogenase

Scope note

  • An enzyme that catalyzes the oxidation of 1-pyrroline-5-carboxylate to L-GLUTAMATE in the presence of NAD. Defects in the enzyme are the cause of hyperprolinemia II.

History note

  • 2006(1981)

In other languages

URI

http://www.yso.fi/onto/mesh/D050842

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