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Concept information

Preferred term

Idiopathic Pulmonary Fibrosis  

Type

  • Topical Descriptor

Broader concept

Entry terms

  • Cryptogenic Fibrosing Alveolitides
  • Cryptogenic Fibrosing Alveolitis
  • Dysplasia, Fibrocystic Pulmonary
  • Fibrocystic Pulmonary Dysplasia
  • Fibrocystic Pulmonary Dysplasias
  • Fibrosing Alveolitides, Cryptogenic
  • Fibrosing Alveolitis, Cryptogenic
  • Idiopathic Fibrosing Alveolitis, Chronic Form
  • Pulmonary Dysplasia, Fibrocystic
  • Pulmonary Fibrosis, Idiopathic

Note

  • PULMONARY FIBROSIS is also available

Scope note

  • A common interstitial lung disease of unknown etiology, usually occurring between 50-70 years of age. Clinically, it is characterized by an insidious onset of breathlessness with exertion and a nonproductive cough, leading to progressive DYSPNEA. Pathological features show scant interstitial inflammation, patchy collagen fibrosis, prominent fibroblast proliferation foci, and microscopic honeycomb change.

History note

  • 2009

In other languages

URI

http://www.yso.fi/onto/mesh/D054990

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