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Concept information

Preferred term

Primary Myelofibrosis  

Type

  • Topical Descriptor

Entry terms

  • Agnogenic Myeloid Metaplasia
  • Agnogenic Myeloid Metaplasias
  • Bone Marrow Fibroses
  • Bone Marrow Fibrosis
  • Chronic Idiopathic Myelofibrosis
  • Fibroses, Bone Marrow
  • Fibrosis, Bone Marrow
  • Idiopathic Myelofibrosis
  • Metaplasia, Agnogenic Myeloid
  • Metaplasia, Myeloid
  • Metaplasias, Agnogenic Myeloid
  • Metaplasias, Myeloid
  • Myelofibroses
  • Myelofibrosis
  • Myelofibrosis With Myeloid Metaplasia
  • Myeloid Metaplasia
  • Myeloid Metaplasia, Agnogenic
  • Myeloid Metaplasias
  • Myeloid Metaplasias, Agnogenic
  • Myeloscleroses
  • Myelosclerosis
  • Myeloses, Nonleukemic
  • Myelosis, Nonleukemic
  • Nonleukemic Myeloses
  • Nonleukemic Myelosis

Scope note

  • A de novo myeloproliferation arising from an abnormal stem cell. It is characterized by the replacement of bone marrow by fibrous tissue, a process that is mediated by CYTOKINES arising from the abnormal clone.

History note

  • 2009

In other languages

URI

http://www.yso.fi/onto/mesh/D055728

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