Concept information
Preferred term
Hereditary Angioedema Type III
Type
-
Topical Descriptor
Broader concept
Entry terms
- Angioedema, Estrogen-Sensitive Hereditary
- Angioedema, Hereditary, Type III
- Angioedemas, Estrogen-Sensitive Hereditary
- Angioneurotic Edema, Hereditary, with Normal C1 Inhibitor Concentration and Function
- Estrogen Related HAE
- Estrogen-Related HAE
- Estrogen-Related HAEs
- Estrogen Sensitive HAE
- Estrogen-Sensitive HAE
- Estrogen-Sensitive HAEs
- Estrogen Sensitive Hereditary Angioedema
- Estrogen-Sensitive Hereditary Angioedema
- Estrogen-Sensitive Hereditary Angioedemas
- HAE, Estrogen-Related
- HAE, Estrogen-Sensitive
- HAEs, Estrogen-Related
- HAEs, Estrogen-Sensitive
- HAE with Normal C1 Inhibitor Concentration and Function
- Hereditary Angioedema, Estrogen-Sensitive
- Hereditary Angioedemas, Estrogen-Sensitive
- Hereditary Angioedema with Normal C1 Inhibitor Activity
Scope note
- A form of hereditary angioedema that occurs in women and is precipitated or worsened by high ESTROGEN levels. It is associated with mutations in the gene for FACTOR XII that result in its increased activity.
History note
- 2010
In other languages
-
Finnish
-
tyypin III HAE
-
tyypin III HANE
-
tyypin III hereditaarinen angioedeema
-
tyypin III hereditaarinen angioneuroottinen edeema
-
tyypin III hereditäärinen angioedeema
-
tyypin III perinnöllinen angioedeema
-
tyypin III perinnöllinen angioödeema
-
tyypin III synnynnäinen angioödeema
-
Swedish
-
Ärftligt angioöedem typ III
-
Östrogenrelaterad HAE
-
Östrogensensitiv hereditär angioödem
URI
http://www.yso.fi/onto/mesh/D056828
{{label}}
{{#each values }} {{! loop through ConceptPropertyValue objects }}
{{#if prefLabel }}
{{/if}}
{{/each}}
{{#if notation }}{{ notation }} {{/if}}{{ prefLabel }}
{{#ifDifferentLabelLang lang }} ({{ lang }}){{/ifDifferentLabelLang}}
{{#if vocabName }}
{{ vocabName }}
{{/if}}