Concept information
Preferred term
Heterotaxy Syndrome
Type
-
Topical Descriptor
Broader concept
Entry terms
- Asplenia Syndrome
- Asplenia Syndromes
- Atrial Isomerism, Left
- Atrial Isomerism, Right
- Atrial Isomerisms, Left
- Atrial Isomerisms, Right
- Heterotaxies, Visceral
- Heterotaxy, Visceral
- Isomerism, Left Atrial
- Isomerism, Right Atrial
- Isomerisms, Left Atrial
- Isomerisms, Right Atrial
- Left Atrial Isomerism
- Left Atrial Isomerisms
- Polysplenia Syndrome
- Polysplenia Syndromes
- Right Atrial Isomerism
- Right Atrial Isomerisms
- Syndrome, Asplenia
- Syndrome, Polysplenia
- Syndromes, Asplenia
- Syndromes, Polysplenia
- Visceral Heterotaxies
- Visceral Heterotaxy
Scope note
- Abnormal thoracoabdominal VISCERA arrangement (visceral heterotaxy) or malformation that involves additional CONGENITAL HEART DEFECTS (e.g., heart isomerism; DEXTROCARDIA) and/or abnormal SPLEEN (e.g., asplenia and polysplenia). Irregularities with the central nervous system, the skeleton and urinary tract are often associated with the syndrome.
History note
- 2012
In other languages
-
Finnish
-
heterotaksiasyndrooma
-
Swedish
-
Asplenia syndrom
-
Höger-isomerism
-
Ivemarks syndrom
-
Polysplenisyndrom
-
Situs ambiguus
-
Vänster-isomerism
URI
http://www.yso.fi/onto/mesh/D059446
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