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Concept information

Preferred term

Kasabach-Merritt Syndrome  

Type

  • Topical Descriptor

Entry terms

  • Hemangioma Thrombocytopenia Syndrome
  • Hemangioma-Thrombocytopenia Syndrome
  • Hemangioma Thrombocytopenia Syndromes
  • Kasabach Merritt Phenomenon
  • Kasabach-Merritt Phenomenon
  • Phenomenon, Kasabach-Merritt
  • Syndrome, Hemangioma Thrombocytopenia
  • Syndromes, Hemangioma Thrombocytopenia
  • Syndromes, Thrombocytopenia-Hemangioma
  • Syndrome, Thrombocytopenia-Hemangioma
  • Thrombocytopenia Hemangioma Syndrome
  • Thrombocytopenia-Hemangioma Syndrome
  • Thrombocytopenia-Hemangioma Syndromes

Scope note

  • Rapidly growing vascular lesion along the midline axis of the neck, upper trunk, and extremities that is characterized by CONSUMPTION COAGULOPATHY; THROMBOCYTOPENIA; and HEMOLYTIC ANEMIA. It is often associated with infantile Kaposiform HEMANGIOENDOTHELIOMA and other vascular tumors such as tufted ANGIOMA.

History note

  • 2012

In other languages

URI

http://www.yso.fi/onto/mesh/D059885

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