Njuike sisdollui

Oza sátnerájus

Sisdoalu giella

Diehtu doahpagis

Ávžžuhuvvon tearbma

Trihexosylceramides  

Tiipa

  • Topical Descriptor

Badjedoaba

Stivrentearpmat

  • Ceramides, Trihexosyl
  • Ceramide Trihexosides
  • Trihexosides, Ceramide
  • Trihexosyl Ceramides

Muituimerkejupmi

  • /biosyn /physiol permitted

Fuomášahttin

  • Glycosphingolipids which contain as their polar head group a trisaccharide (galactose-galactose-glucose) moiety bound in glycosidic linkage to the hydroxyl group of ceramide. Their accumulation in tissue, due to a defect in ceramide trihexosidase, is the cause of angiokeratoma corporis diffusum (FABRY DISEASE).

Fuomášahttin rievdadanhistorjjás

  • 91(79); was see under GLYCOSPHINGOLIPIDS 1979-90

Eará gielain

URI

http://www.yso.fi/onto/mesh/D014281

Luđe dán doahpaga:

RDF/XML TURTLE JSON-LD Ráhkaduvvon 5/16/78, maŋimuš rievdaduvvon 7/5/06